Seminars in Pediatric Neurology
Volume 17, Issue 1 , Pages 17-23 , March 2010

Transient Axial Hypotonia and Alteration of Consciousness in an Infant With Chiari I Malformation

  • Olga Fishman

      Affiliations

    • Saul R. Korey Department of Neurology, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • The Montefiore/Einstein Epilepsy Center, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • Corresponding Author InformationAddress reprint requests to Olga Fishman, MD, EEG Laboratory, Department of Neurology, Montefiore Medical Center, 111 East 210th St, Bronx, NY 10467
    • ,
  • Yoshimi Sogawa

      Affiliations

    • Saul R. Korey Department of Neurology, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • Department of Pediatrics, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • The Dominick P. Purpura Department of Neuroscience, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • ,
  • S.L. Moshé

      Affiliations

    • Saul R. Korey Department of Neurology, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY
    • The Dominick P. Purpura Department of Neuroscience, Albert Einstein College of Medicine and Montefiore Medical Center, Bronx, NY

References 

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  4. Nishino S. Clinical and neurobiological aspects of narcolepsy. Sleep Med. 2007;8:373–399
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  13. Tubbs RS, Lyerly MJ, Loukas M, et al. The pediatric Chiari I malformation: A review. Childs Nerv Syst. 2007;23:1239–1250
  14. Nohria V, Oakes WJ. Chiari I malformation: A review of 43 patients. Pediatr Neurosurg. 1990;16:222–227
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  17. Schaul N, Gloor P, Gotman J. The EEG in deep midline lesions. Neurology. 1981;31:157–167
  18. Pandey A, Robinson S, Cohen AR. Cerebellar fits in children with Chiari I malformation. Neurosurg Focus. 2001;11:E4
  19. Korff CM, Nordli DR. The clinical-electrographic expression of infantile seizures. Epilepsy Res. 2006;70(suppl 1):S116–S131
  20. Hamer HM, Wyllie E, Luders HO, et al. Symptomatology of epileptic seizures in the first three years of life. Epilepsia. 1999;40:837–844
  21. Fogarasi A, Jokeit H, Faveret E, et al. The effect of age on seizure semiology in childhood temporal lobe epilepsy. Epilepsia. 2002;43:638–643
  22. Fogarasi A, Boesebeck F, Tuxhorn I. A detailed analysis of symptomatic posterior cortex seizure semiology in children younger than seven years. Epilepsia. 2003;44:89–96
  23. Iannetti P, Spalice A, De Felice Ciccoli C, et al. Seizures in paediatric Chiari type I malformation: The role of single-photon emission computed tomography. Acta Paediatr. 2002;91:313–317
  24. Elia M, Biondi R, Sofia V, et al. Seizures in Chiari I malformation: A clinical and electroencephalographic study. J Child Neurol. 1999;14:446–450
  25. Brill CB, Gutierrez J, Mishkin MM. Chiari I malformation: Association with seizures and developmental disabilities. J Child Neurol. 1997;12:101–106
  26. Buoni S, Zannolli R, di Bartolo RM, et al. Surgery removes EEG abnormalities in patients with Chiari type I malformation and poor CSF flow. Clin Neurophysiol. 2006;117:959–963

 Supported by NINDS grant NS-43209 and the Heffer Family Medical Foundation.

 S.L.M. is the recipient of the Martin A. and Emily L. Fisher fellowship in Neurology and Pediatrics.

PII: S1071-9091(10)00007-0

doi: 10.1016/j.spen.2010.01.006

Seminars in Pediatric Neurology
Volume 17, Issue 1 , Pages 17-23 , March 2010

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